Surgical management of labial hypertrophy in Sturge weber syndrome
Author(s): Sarra Benwadih, Maha Bouksirat, Kenza Sadki, Dani Bouchra and Boulaadas Malik
Abstract:
Sturge Weber Syndrome (SWS) is a rare neurocutaneous vascular disorder characterized by a facial
birthmark known as a Port Wine Stain (PWS), eye abnormalities, and abnormal blood vessels in the
brain. It is basically a multisystem disorder that can involve the nervous system, skin, and eyes
(phakomatosis). The broad array of clinical manifestations and potentially life-threatening
complications underscores the crucial and imperative need for an accurate diagnosis. An effective
treatment strategy for SWS patients involves a multidisciplinary approach. Dental procedures in these
individuals pose challenges due to the potential risk for substantial bleeding during both intra- and
postoperative phases.
This article aims to document a case of a 27 year old woman and a 24 year old man diagnosed with
Sturge weber syndrome at birth and presented a labial hypertrophy.